MYOPERICYTOMA OF THE SOFT TISSUE IN THE LOWER EXTREMITIES: CLINICAL CASE AND LITERATURE REVIEW

  • Rodica Sanziana Cusu University of Medicine and Pharmacy Carol Davila
  • Josep Maria Parcet Riu
  • Francisco Herrero Fernandez
Keywords: myopericitoma, spindle cells, VY perforator flap

Abstract

The perivascular myoid tumors are a group of tumors which contains myopericitoma, a variant of the glomic tumor which is a rare neoplasm of the soft tissues. Currently there are less than 200 cases of benign tumors described in the literature. Although the term was only accepted by WHO in 2012 the first case was documented as early as 1998. Most of the cases reported were bening and appeared as nodular and painless. We present a case of a 60 year old man who had the preliminary diagnosis of a cyst in the subdermis of the lower leg. When excision was intented by the general practicioner the results were bleeding and induration. He was corectly diagnosed after biopsy with myopericitoma. Microscopically the tumor was composed of uniform spindle and ovoid cells with no atypies, arranged concentrically around the blood vessels. The tumor cells were diffusively positive for smooth muscle actin. The surgeons performed excision of the lesion and the defect was reconstructed by a VY perforator flap based on the tibial posterior perforator artery. The VY advancement flap apart from having the benefit of being aesthetic it also allows the region to maintain sensation which in this case was especially important with the lower leg being more exposed to small hits and injury.

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Published
2021-12-20
How to Cite
[1]
R. Cusu, J. Parcet Riu, and F. Fernandez, “MYOPERICYTOMA OF THE SOFT TISSUE IN THE LOWER EXTREMITIES: CLINICAL CASE AND LITERATURE REVIEW”, JSS, vol. 8, no. 3, Dec. 2021.