LARYNGEAL SYNOVIAL SARCOMA – A CASE REPORT

  • Alexandru Nicolae Vlăescu ENT Department, Doctoral School, University of Medicine and Pharmacy of Craiova, Romania
  • Elena Ioniță ENT Department, University of Medicine and Pharmacy of Craiova, Romania & ENT Clinic, Emergency County Hospital Craiova, Romania
  • Andreea Nicoleta Vlăescu ENT Department, Doctoral School, University of Medicine and Pharmacy of Craiova, Romania
  • Florin Anghelina ENT Department, University of Medicine and Pharmacy of Craiova, Romania & ENT Clinic, Emergency County Hospital Craiova, Romania
  • Iulică Ioniță ENT Clinic, Emergency County Hospital Craiova, Romania
  • Carmen Aurelia Mogoantă ENT Department, University of Medicine and Pharmacy of Craiova, Romania & ENT Clinic, Emergency County Hospital Craiova, Romania
  • Mircea Sorin Ciolofan ENT Department, University of Medicine and Pharmacy of Craiova, Romania & ENT Clinic, Emergency County Hospital Craiova, Romania
Keywords: larynx, synovial sarcoma, total laryngectomy, rare tumors

Abstract

Laryngeal synovial sarcoma is an extremely rare mesenchymal tumor. During the past four decades, literature findings revealed under 40 cases with this localization. We are bringing forward the case of a 70-year-old male patient who was referred to the ENT Clinic as a respiratory emergency – a tumor obstructing the laryngeal glottis, for which an emergency tracheotomy was initially performed, followed by a CT scan and a biopsy under general anesthesia through suspension videolaringoscopy. The histopathological report was suggestive of a biphasic synovial sarcoma. A multidisciplinary team set the surgical indication for total laryngectomy followed by chemo-radiotherapy. Long-term follow-up is mandatory for recurrence prevention. Patient has checked in for follow-up every 3 months over the past 2 years, with no macroscopic signs of tumoral relapse.

References

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Published
2020-12-26
How to Cite
[1]
A. Vlăescu, “LARYNGEAL SYNOVIAL SARCOMA – A CASE REPORT”, JSS, vol. 7, no. 3, pp. 110-113, Dec. 2020.